To date, little is known about sensory processing in Williams syndrome (WS) and the similarities of the sensory profile in individuals with WS compared to people with other neurodevelopmental disorders. The current review aims to consolidate available evidence on sensory processing in WS. Eighteen primary studies investigating sensory processing in individuals with WS were identified through systematic searches of electronic databases. Fourteen studies investigated hyperacusis (sound sensitivity) in WS and four papers examined broader sensory processing characteristics. A high prevalence of both hyperacusis and sensory processing difficulties were reported. These were associated with younger age, more behavioural problems and a greater severity of other clinical symptoms and were discriminant between other developmental disorders and typically developing samples.