Turner syndrome (TS) is a chromosomal disorder, caused by either complete or partial X monosomy (i.e., absence of one member of a pair of chromosomes) in some or all cells. It affects approximately 1 in 2,500 female live births. However, only about 1% of fetuses with 45, X karyotype (image of one's chromosomes) are carried to term, and up to 10% of spontaneous miscarriages are found to have a 45, X karyotype (Saenger et al., 2001). A number of articles have been published about topics such as medication management, diagnosis, and cardiovascular concerns (Davenport, 2010; Gravholt et al., 2019; Lyon et al., 1985), and research is emerging in the area of behavioral and psychological considerations for those with TS (see Hong et al., 2011; Lepage et al., 2013). This article will present an overview of TS in terms of diagnosis and symptoms. Then, the primary focus of the article will be to review developmental and behavioral concerns present in girls with TS and discuss how school psychologists can help support this population in the education system.