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The Executive Function Account of Repetitive Behavior: Evidence from Rubinstein-Taybi Syndrome
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Waite, Jane; Beck, Sarah R.; Powis, Laurie; Oliver, Chris – American Journal on Intellectual and Developmental Disabilities, 2023
In this study, we focus on Rubinstein-Taybi syndrome (RTS) to explore the associations between executive function deficits and repetitive behaviors. Thirty individuals with RTS completed direct assessments of inhibition, working memory and set-shifting. Informants completed repetitive behavior and executive function questionnaires. Repetitive…
Descriptors: Executive Function, Repetition, Behavior Problems, Genetic Disorders
Block Design Performance in Williams Syndrome: Visuospatial Abilities or Task Approach Skills?
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Block, Elisa; Farran, Emily K.; Van Herwegen, Jo – American Journal on Intellectual and Developmental Disabilities, 2022
The block design task (BDT) is a visuospatial measure that individuals with Williams syndrome (WS) perform poorly on. However, it is unclear what underlies their impaired performance. This study investigated whether poorer performance is a result of visuospatial difficulties, executive function (EF) difficulties, atypical looking strategies, or a…
Descriptors: Task Analysis, Visual Perception, Spatial Ability, Executive Function
The "FMR1" Premutation Phenotype and Mother-Youth Synchrony in Fragile X Syndrome
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Moser, Carly; Mattie, Laura; Abbeduto, Leonard; Klusek, Jessica – American Journal on Intellectual and Developmental Disabilities, 2021
A subset of mothers who carry the "FMR1" premutation may express a unique phenotype. The relationship between the "FMR1" phenotype and mother-child interaction in families with fragile X-associated disorders has not been well characterized, despite the importance of high-quality mother-child interaction for child development.…
Descriptors: Mothers, Genetic Disorders, Interaction, Adolescents
Executive Functioning Mediates the Effect of Behavioral Problems on Depression in Mothers of Children with Developmental Disabilities
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Chan, Wai; Smith, Leann E.; Greenberg, Jan S.; Hong, Jinkuk; Mailick, Marsha R. – American Journal on Intellectual and Developmental Disabilities, 2017
The present investigation explored long-term relationships of behavioral symptoms of adolescents and adults with developmental disabilities with the mental health of their mothers. Fragile X premutation carrier mothers of an adolescent or adult child with fragile X syndrome (n = 95), and mothers of a grown child with autism (n = 213) were…
Descriptors: Behavior Problems, Adolescents, Adults, Genetic Disorders
Executive Functions and Prader-Willi Syndrome: Global Deficit Linked with Intellectual Level and Syndrome-Specific Associations
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Chevalère, Johann; Postal, Virginie; Jauregui, Joseba; Copet, Pierre; Laurier, Virginie; Thuilleaux, Denise – American Journal on Intellectual and Developmental Disabilities, 2015
The aim of this study was to support the growing evidence suggesting that Prader-Willi Syndrome (PWS) might present with an impairment of executive functions (EFs) and to investigate whether this impairment is specific to patients with PWS or due to their intellectual disability (ID). Six tasks were administered to assess EFs (inhibition,…
Descriptors: Genetic Disorders, Disabilities, Executive Function, Neurological Impairments
Social Cognition in Adolescent Girls with Fragile X Syndrome
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Turkstra, Lyn S.; Abbeduto, Leonard; Meulenbroek, Peter – American Journal on Intellectual and Developmental Disabilities, 2014
This study aimed to characterize social cognition, executive functions (EFs), and everyday social functioning in adolescent girls with fragile X syndrome, and identify relationships among these variables. Participants were 20 girls with FXS and 20 age-matched typically developing peers. Results showed significant between-groups differences in…
Descriptors: Executive Function, Social Cognition, Interpersonal Competence, Females