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The Topographies and Operant Functions of Challenging Behaviours in Fragile X Syndrome: A Systematic Review and Analysis of Existing Data
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Hardiman, Rebecca Lyndsey; McGill, Peter – Journal of Intellectual & Developmental Disability, 2017
Background: Challenging behaviour, such as self-injury and physical aggression, is an issue of concern regarding a high proportion of individuals with fragile X syndrome. The aim of this review was to provide a comprehensive overview of the topographies and operant functions of challenging behaviours within the syndrome. Method: Five electronic…
Descriptors: Behavior Problems, Genetic Disorders, Aggression, Self Destructive Behavior
Mother-Child Dyadic Co-Regulation in Children with Intellectual Disability: A Comparison among Dyads with Children with Chromosome 14 Aberrations, Down Syndrome and Typical Development
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Zampini, Laura; Zanchi, Paola – Journal of Intellectual & Developmental Disability, 2020
Background: The present study aimed at investigating mother-child dyadic co-regulation patterns in dyads with children with intellectual disability (ID). Method: 24 children paired for developmental age and vocabulary size (8 with chromosome 14 aberrations, 8 with Down syndrome, and 8 with typical development) and their mothers participated in the…
Descriptors: Mothers, Parent Child Relationship, Genetic Disorders, Down Syndrome
Service Receipt of Adults with Rare Genetic Syndromes Who Engage in Challenging Behaviour
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Awan, N.; Oliver, C.; Wilde, L.; Eden, K.; Waite, J. – Journal of Intellectual & Developmental Disability, 2018
Background: There is limited research documenting the health and/or psychological services accessed by adults with rare genetic syndromes who engage in challenging behaviour. The study documented service receipt and associations with person characteristics. Method: Thirty-two parents of adults with rare genetic syndromes completed an adapted…
Descriptors: Adults, Genetic Disorders, Behavior Problems, Autism
Extrapyramidal Symptoms and Medication Use in Mucopolysaccharidosis Type III
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Tchan, Michel C.; Sillence, David – Journal of Intellectual & Developmental Disability, 2009
Background: We report the case of a 16-year-old male with Mucopolysaccharidosis III type A (Sanfilippo syndrome) who was commenced on risperidone for behaviour management. He rapidly developed extrapyramidal symptoms that have not resolved. Method: The medication histories of 20 patients with Mucopolysaccharidosis III seen at a Lysosomal Storage…
Descriptors: Incidence, Patients, Drug Therapy, Symptoms (Individual Disorders)
Maternal Parenting Stress in Families with a Child with Angelman Syndrome or Prader-Willi Syndrome
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Wulffaert, Josette; Scholte, Evert M.; Van Berckelaer-Onnes, Ina A. – Journal of Intellectual & Developmental Disability, 2010
Background: Parenting stress was investigated in mothers with a child with Angelman syndrome (AS) or Prader-Willi syndrome (PWS), which are genetically related. Method: Mothers of 24 children with AS and 23 children with PWS (2-12 years) completed the Nijmegen Parenting Stress Index-Short, Developmental Behaviour Checklist, and Vineland Screener…
Descriptors: Mothers, Mental Retardation, Family Programs, Child Rearing
Observing the Behaviour and Interactions of Adults with Congenital Deafblindness Living in Community Residences
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Prain, Meredith; McVilly, Keith; Ramcharan, Paul; Currie, Sally; Reece, John – Journal of Intellectual & Developmental Disability, 2010
Background: Adults with congenital deafblindness (CDB) have received little attention from researchers. In this study we examined the nature of interactions between adults with CDB and the staff who mediate their support, and investigated the reliability of an observation coding system, originally designed for observing adults with severe…
Descriptors: Observation, Interrater Reliability, Interpersonal Relationship, Group Homes