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Systematic Review of Intervention Programs Designed to Improve the Socioemotional Skills of Children and Adolescents with Prader-Willi Syndrome
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Ane Perosanz; Oscar Martínez; Néstor Roselli; Paula Pérez-Núñez; Samuel Anguiano; Juan Francisco López-Paz – American Journal on Intellectual and Developmental Disabilities, 2025
The present study is a systematic review of intervention programs designed to improve the socioemotional skills of children and adolescents with Prader-Willi syndrome (PWS). The search was conducted in the Web of Science and Pubmed databases following the PRISMA guidelines. A total of six studies made up the final sample and were organized based…
Descriptors: Genetic Disorders, Intervention, Interpersonal Competence, Emotional Response
Social Management Training in Males with 47,XXY (Klinefelter Syndrome): A Pilot Study of a Neurocognitive-Behavioral Treatment Targeting Social, Emotional, and Behavioral Problems
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Martin, Francien; van Rijn, Sophie; Bierman, Marit; Swaab, Hanna – American Journal on Intellectual and Developmental Disabilities, 2021
Klinefelter syndrome (47,XXY) is associated with problems in social interaction and behavioral adaptation. Sixteen adolescents and adult men with 47,XXY enrolled in a pilot-study evaluating the effectiveness of Social Management Training (SMT), a novel neurocognitive-behavioral treatment program targeted at improving social, emotional, and…
Descriptors: Genetic Disorders, Adolescents, Adults, Males
Differential Relationships of Anxiety and Autism Symptoms on Social Skills in Young Boys with Fragile X Syndrome
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Reisinger, Debra L.; Roberts, Jane E. – American Journal on Intellectual and Developmental Disabilities, 2017
Social skills are critical for academic, social, and psychological success of children with both typical and atypical development. Boys with fragile X syndrome (FXS) are at high risk for social skill impairments, given intellectual impairments and secondary conditions. The present study examines the impact of adaptive behavior, autism symptoms,…
Descriptors: Anxiety, Autism, Symptoms (Individual Disorders), Males
A Psychometric Evaluation of the Motor-Behavioral Assessment Scale for Use as an Outcome Measure in Rett Syndrome Clinical Trials
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Raspa, Melissa; Bann, Carla M.; Gwaltney, Angela; Benke, Timothy A.; Fu, Cary; Glaze, Daniel G.; Haas, Richard; Heydemann, Peter; Jones, Mary; Kaufmann, Walter E.; Lieberman, David; Marsh, Eric; Peters, Sarika; Ryther, Robin; Standridge, Shannon; Skinner, Steven A.; Percy, Alan K.; Neul, Jeffrey L. – American Journal on Intellectual and Developmental Disabilities, 2020
Rett syndrome (RTT) is a neurodevelopmental disorder that primarily affects females. Recent work indicates the potential for disease modifying therapies. However, there remains a need to develop outcome measures for use in clinical trials. Using data from a natural history study (n = 1,075), we examined the factor structure, internal consistency,…
Descriptors: Genetic Disorders, Psychometrics, Psychomotor Skills, Physical Disabilities
The PRETEND Program: Evaluating the Feasibility of a Remote Parent-Training Intervention for Children with Prader-Willi Syndrome
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Zyga, Olena; Russ, Sandra W.; Dimitropoulos, Anastasia – American Journal on Intellectual and Developmental Disabilities, 2018
Research has shown that children with Prader-Willi syndrome (PWS) have social-cognitive challenges and decreased quality parent-child interactions. However, given the low prevalence rate, developing interventions for children with PWS is faced with the significant challenge of enrolling enough participants for local studies. To better understand…
Descriptors: Genetic Disorders, Intellectual Disability, Interpersonal Competence, Parent Child Relationship
Social Approach and Emotion Recognition in Fragile X Syndrome
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Williams, Tracey A.; Porter, Melanie A.; Langdon, Robyn – American Journal on Intellectual and Developmental Disabilities, 2014
Evidence is emerging that individuals with Fragile X syndrome (FXS) display emotion recognition deficits, which may contribute to their significant social difficulties. The current study investigated the emotion recognition abilities, and social approachability judgments, of FXS individuals when processing emotional stimuli. Relative to…
Descriptors: Genetic Disorders, Mental Retardation, Emotional Response, Interpersonal Competence
Parent and Teacher Perspectives about Problem Behavior in Children with Williams Syndrome
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Klein-Tasman, Bonita P.; Lira, Ernesto N.; Li-Barber, Kirsten T.; Gallo, Frank J.; Brei, Natalie G. – American Journal on Intellectual and Developmental Disabilities, 2015
Problem behavior of 52 children with Williams syndrome ages 6 to 17 years old was examined based on both parent and teacher report. Generally good inter-rater agreement was found. Common areas of problem behavior based both on parent and teacher report included attention problems, anxiety difficulties, repetitive behaviors (e.g., obsessions,…
Descriptors: Behavior Problems, Genetic Disorders, Children, Adolescents
Adaptive Behavior and Problem Behavior in Young Children with Williams Syndrome
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Hahn, Laura J.; Fidler, Deborah J.; Hepburn, Susan L. – American Journal on Intellectual and Developmental Disabilities, 2014
The present study compares the adaptive behavior profile of 18 young children with Williams syndrome (WS) and a developmentally matched group of 19 children with developmental disabilities and examines the relationship between adaptive behavior and problem behaviors in WS. Parents completed the Vineland Adaptive Behavioral Scales--Interview…
Descriptors: Genetic Disorders, Behavior Problems, Young Children, Comparative Analysis
Social Cognition in Adolescent Girls with Fragile X Syndrome
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Turkstra, Lyn S.; Abbeduto, Leonard; Meulenbroek, Peter – American Journal on Intellectual and Developmental Disabilities, 2014
This study aimed to characterize social cognition, executive functions (EFs), and everyday social functioning in adolescent girls with fragile X syndrome, and identify relationships among these variables. Participants were 20 girls with FXS and 20 age-matched typically developing peers. Results showed significant between-groups differences in…
Descriptors: Executive Function, Social Cognition, Interpersonal Competence, Females
Exploring the Adult Life of Men and Women with Fragile X Syndrome: Results from a National Survey
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Hartleyand, Sigan L.; Seltzer, Marsha Mailick; Raspa, Melissa; Olmstead, Murrey; Bishop, Ellen; Bailey, Donald B., Jr. – American Journal on Intellectual and Developmental Disabilities, 2011
Using data from a national family survey, the authors describe the adult lives (i.e., residence, employment, level of assistance needed with everyday life, friendships, and leisure activities) of 328 adults with the full mutation of the FMR1 gene and identify characteristics related to independence in these domains. Level of functional skills was…
Descriptors: Genetic Disorders, Mental Retardation, Adults, National Surveys
Autism Spectrum Disorder in Children and Adolescents with Fragile X Syndrome: Within-Syndrome Differences and Age-Related Changes
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McDuffie, Andrea; Abbeduto, Leonard; Lewis, Pamela; Kover, Sara; Kim, Jee-Seon; Weber, Ann; Brown, W. Ted – American Journal on Intellectual and Developmental Disabilities, 2010
The Autism Diagnostic Interview-Revised (ADI-R) was used to examine diagnostic profiles and age-related changes in autism symptoms for a group of verbal children and adolescents who had fragile X syndrome, with and without autism. After controlling for nonverbal IQ, we found statistically significant between-group differences for lifetime and…
Descriptors: Autism, Interests, Intelligence Quotient, Interaction